Outline
- Introduction
- Epidemiology
- Associated Syndromes
- Clinical Presentation
- Pathological Classification
- Diagnosis and DDx
- Clinical staging and prognosis
- Treatment
- Soft tissue sarcoma in pediatric divided to:
- Rhabdomyosarcoma (40-50%)
- Non-rhabdomyosarcoma (synovial sarcoma, fibrosarcoma, PNET)
- Soft tissue sarcoma common in adult
- Rhabdomyosarcoma: malignant mesenchymal tumor of striated skeletal muscle
Epidemiology
- 3-4% of all child cancer
- 4 cases per million in Canada
- Conmonest STT in patient <20 Y.O
- M:F(I,5:I)
- Two third of cases diagnosed in first 5 years
- Specific risk factor---unknown and most cases are sporadic
- 20% have lung metastases at time of presentation
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